Gorlin-Goltz Syndrome: Case Report and Review

The Gorlin-Goltz syndrome or (the nevoid basal cell carcinoma syndrome) is a rare autosomal dominant syndrome with multiple organ involvements. The common manifestations include multiple odontogenic keratocysts in the jaws, multiple basal cell nevi on the skin with an early age onset, palmar pits, bifid or splayed ribs, high arched palate, euryopia, areas of hyper-pigmentation in the upper eyelid of left eye and dorsal surface of hands, calcified diaphragma sellae, and calcifications of the falx cerebri. In this case report, we report the only case of Gorlin-Goltz syndrome in the Jammu-Kashmir region in a young 20-year-old female patient.