Gorlin-Goltz Syndrome: Case Report and Review

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Case Report | | Volume 10 Issue 1 (January-March, 2021) | Pages 4 - 7

Gorlin-Goltz Syndrome: Case Report and Review

Tahir Ahmad

Parveen Akhter Lone

Javaid Ahmed Wani

Nusrat Rafi

Department of Oral and Maxillo Facial Surgey, Indra Gandi Government Dental College, Jammu and Kashmir

SRI Venkateswara University, Uttar Pradesh, India

Under a Creative Commons license

Open Access

Received

Jan. 22, 2020

Accepted

April 22, 2020

Published

June 30, 2020

Abstract

The Gorlin-Goltz syndrome or (the nevoid basal cell carcinoma syndrome) is a rare autosomal dominant syndrome with multiple organ involvements. The common manifestations include multiple odontogenic keratocysts in the jaws, multiple basal cell nevi on the skin with an early age onset, palmar pits, bifid or splayed ribs, high arched palate, euryopia, areas of hyper-pigmentation in the upper eyelid of left eye and dorsal surface of hands, calcified diaphragma sellae, and calcifications of the falx cerebri. In this case report, we report the only case of Gorlin-Goltz syndrome in the Jammu-Kashmir region in a young 20-year-old female patient.

Keywords

Gorlin-Goltz; Basal Cell; Bifid Ribs; Odontogenic Keratocyst