Klippel Trenaunay Syndrome: A Rare Vascular Disorder

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Case Report | | Volume 10 Issue 2 (October-December, 2021) | Pages 6 - 9

Klippel Trenaunay Syndrome: A Rare Vascular Disorder

Aun Ali

Dileep Kumar

Summaya Saeed

Khursheed Ahmed Samoo

Amjad Siraj Memon

Department of Surgery, Civil Hospital Karachi, Dow University of Health Sciences, Karachi, Pakistan

Department of Surgery, Jinnah Medical Dental College, Karachi, Pakistan

Under a Creative Commons license

Open Access

Received

April 6, 2021

Accepted

Aug. 11, 2021

Published

Dec. 31, 2021

Abstract

Klippel-Trenaunay-syndrome (KTS) is a rare vascular disorder consisting of a triad of features including capillary malformations, varicose veins and soft tissue abnormalities. It overlaps with few other rare vascular disorders such as ‘Sturge Weber syndrome’ and ‘Parks Weber syndrome’ with few notable distinguishing features. The diagnosis is clinical, however, imaging is necessary for confirmation. The treatment is conservative and individualized. In this case report, we present a variant of KTS which demonstrates only two of the three features.

Keywords

Klippel Trenaunay Syndrome; Capillary Malformations; Varicose Veins; Sturge Weber Syndrome; Parks Weber Syndrome