Klippel-Trenaunay-syndrome (KTS) is a rare vascular disorder consisting of a triad of features including capillary malformations, varicose veins and soft tissue abnormalities. It overlaps with few other rare vascular disorders such as ‘Sturge Weber syndrome’ and ‘Parks Weber syndrome’ with few notable distinguishing features. The diagnosis is clinical, however, imaging is necessary for confirmation. The treatment is conservative and individualized. In this case report, we present a variant of KTS which demonstrates only two of the three features.